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Case Report | Open Access

Progressive Conductive Hearing Loss in Osteogenesis Imperfecta (Lobstein Disease): A Case Report

Karim Messaoudi1( ), Nassim Ait Mesbah2, Nadia Yahi2
Department of Medicine, Faculty of Medicine, University of Kasdi Merbah, Ouargla 30000, Algeria
Department of Medicine, University of Algiers 1, Algiers, Algeria
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Abstract

Background

Osteogenesis imperfecta (OI), also known as Lobstein disease, is a rare inherited connective tissue disorder characterized by bone fragility and various extra-skeletal manifestations. Hearing loss is a frequent but often underestimated complication that may significantly impair quality of life.

Case presentation

We report the case of a 34-year-old woman with clinically established osteogenesis imperfecta type I who developed progressive bilateral conductive hearing loss over a three-year period. Audiological evaluation revealed symmetrical conductive impairment with preserved speech discrimination. High-resolution temporal bone computed tomography (CT) demonstrated diffuse otic capsule demineralization, bilateral stapes footplate thickening, and atypical crown-shaped hypodense lesions surrounding the cochlea.

Conclusion

Early recognition of hearing loss in osteogenesis imperfecta, combined with detailed imaging and multidisciplinary management, is essential to optimize functional outcomes.

Keywords

osteogenesis imperfectalobstein diseaseconductive hearing losstemporal bone CTcase report

References

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Journal of Otology
Volume 21 Issue 2,
April 2026
Pages 87-89
DOI: 10.26599/JOTO.2026.9540057

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Cite this article:
Messaoudi K, Ait Mesbah N, Yahi N. Progressive Conductive Hearing Loss in Osteogenesis Imperfecta (Lobstein Disease): A Case Report. Journal of Otology, 2026, 21(2): 87-89. https://doi.org/10.26599/JOTO.2026.9540057

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Received: 18 July 2025
Revised: 04 February 2026
Accepted: 09 February 2026
Published: 29 April 2026
© 2026 PLA General Hospital Department of Otolaryngology Head and Neck Surgery. Publishing services by Tsinghua University Press.

This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).