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Journal of Neurorestoratology 2020, 8(2): 83-92 https://doi.org/10.26599/JNR.2020.9040010
Review Article | Open Access | Issue | Published: 04 August 2020

Chinese expert consensus on diagnosis and management of split cord malformation

Show Author's Information Bo Xiu1( ),  Fuyun Liu2,  Aijia Shang3,  Rui Zhang4
Department of Neurosurgery, The 7th Medical Center of PLA General Hospital, Beijing 100700, China
Department of Pediatric Orthopaedics, Zhengzhou University The 3rd Hospital, Zhengzhou 450052, Henan, China
Department of Neurosurgery, The 1st Medical Center of PLA General Hospital, Beijing 100853, China
Department of Neurosurgery, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Ji'nan 250021, Shandong, China
Keywords:
split cord malformation, tethered cord syndrome, neural tube defect, diagnosis, surgery, consensus
Cite this article:
Xiu B, Liu F, Shang A, et al. Chinese expert consensus on diagnosis and management of split cord malformation. Journal of Neurorestoratology, 2020, 8(2): 83-92. https://doi.org/10.26599/JNR.2020.9040010
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Abstract Full text About this article

Split cord malformation (SCM) is a neural tube defect that the spinal cord is longitudinally separated into two hemicords with individual functions, which causes severe spinal cord impairment and sensorimotor deficit. As a kind of myelodysplasia and a special type of tethered cord syndrome, SCM is not widely understood, and common issues in the diagnosis and treatment of SCM should be clarified. In this paper, the Chinese Split Cord Malformation Working Group made a consensus for SCM on embryopathogenesis and types, clinical presentations, neuroimaging assessment, indications and principle of the surgery, surgical techniques and nuances, and prognosis and follow up.


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About this article

Chinese expert consensus on diagnosis and management of split cord malformation

Show Author's information Bo Xiu1( ), Fuyun Liu2, Aijia Shang3, Rui Zhang4
Department of Neurosurgery, The 7th Medical Center of PLA General Hospital, Beijing 100700, China
Department of Pediatric Orthopaedics, Zhengzhou University The 3rd Hospital, Zhengzhou 450052, Henan, China
Department of Neurosurgery, The 1st Medical Center of PLA General Hospital, Beijing 100853, China
Department of Neurosurgery, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Ji'nan 250021, Shandong, China

Abstract

Split cord malformation (SCM) is a neural tube defect that the spinal cord is longitudinally separated into two hemicords with individual functions, which causes severe spinal cord impairment and sensorimotor deficit. As a kind of myelodysplasia and a special type of tethered cord syndrome, SCM is not widely understood, and common issues in the diagnosis and treatment of SCM should be clarified. In this paper, the Chinese Split Cord Malformation Working Group made a consensus for SCM on embryopathogenesis and types, clinical presentations, neuroimaging assessment, indications and principle of the surgery, surgical techniques and nuances, and prognosis and follow up.

Keywords: split cord malformation, tethered cord syndrome, neural tube defect, diagnosis, surgery, consensus

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Received: 26 April 2020
Revised: 03 June 2020
Accepted: 24 June 2020
Published: 04 August 2020
Issue date: June 2020

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© The authors 2020

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This article is published with open access at http://jnr.tsinghuajournals.com

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