@article{Messaoudi2026, 
author = {Karim Messaoudi and Nassim Ait Mesbah and Nadia Yahi},
title = {Progressive Conductive Hearing Loss in Osteogenesis Imperfecta (Lobstein Disease): A Case Report},
year = {2026},
journal = {Journal of Otology},
volume = {21},
number = {2},
pages = {87-89},
keywords = {osteogenesis imperfecta, lobstein disease, conductive hearing loss, temporal bone CT, case report},
url = {https://www.sciopen.com/article/10.26599/JOTO.2026.9540057},
doi = {10.26599/JOTO.2026.9540057},
abstract = {Background Osteogenesis imperfecta (OI), also known as Lobstein disease, is a rare inherited connective tissue disorder characterized by bone fragility and various extra-skeletal manifestations. Hearing loss is a frequent but often underestimated complication that may significantly impair quality of life. Case presentation We report the case of a 34-year-old woman with clinically established osteogenesis imperfecta type I who developed progressive bilateral conductive hearing loss over a three-year period. Audiological evaluation revealed symmetrical conductive impairment with preserved speech discrimination. High-resolution temporal bone computed tomography (CT) demonstrated diffuse otic capsule demineralization, bilateral stapes footplate thickening, and atypical crown-shaped hypodense lesions surrounding the cochlea. Conclusion Early recognition of hearing loss in osteogenesis imperfecta, combined with detailed imaging and multidisciplinary management, is essential to optimize functional outcomes.}
}